Intracranial arachnoid cyst (IAC) is a type of intracranial space-occupying lesion resulting from the accumulation of cerebrospinal fluid in the arachnoid membrane, either congenitally or acquired. The majority of cases are asymptomatic, while a minority may present with symptoms such as headache, cognitive impairment and epilepsy. Epilepsy is a common neurological disorder that can cause significant disease burden due to recurrent seizures. Currently, the association between arachnoid cysts and epilepsy remains unclear, and the optimal treatment approach is controversial. This article aims to provide a comprehensive review of the epidemiology, clinical features, pathogenesis, auxiliary examination, and treatment of Arachnoid cyst complicated by epilepsy, with the goal of enhancing our understanding of this condition.