This article reports a case of intracranial and extracranial communicating epithelioid sarcoma involving the occipital lobe and the occipitalia scalp. The male patient， aged 22 years， had headache and blurred vision for more than one month. He had a history of surgery for right occipital subcutaneous epithelioid sarcoma. Pathological examination showed that the tumor was multinodular with fibrous tissue compressed between the nodules to form pseudomembrane； hemorrhage， granuloma-like structure， and hematogenous metastasis and were observed in tumor tissue； immunohistochemical staining showed that EMA， CK-pan， and CD34 were expressed in tumor cells， while INI-1， CK7， and CD117 were not expressed. The patient was diagnosed with the recurrence of epithelioid sarcoma with hematogenous brain metastasis. ［Journal of International Neurology and Neurosurgery, 2023, 50(4): 40-43］