Spinal myoclonus is a relatively rare type of myoclonus, which can be caused by various primary or secondary spinal cord lesions. It has complex manifestations and is difficult to identify and treat. According to the origin and mode of transmission, it is mainly divided into propriospinal myoclonus and spinal segmental myoclonus. A systematic comparison of the clinical manifestations, etiology, pathogenesis, diagnosis, and treatment between the two will provide guidance for clinical practice. This article reviews the progress in relevant clinical research.